[Cystic fibrosis: now and in the future]

The paper describes the genetic and pathophysiological basis of cystic fibrosis. The most frequent manifestations of the disease are listed and the currently available therapeutic options, both causal and symptomatic, are presented. Special emphasis is placed on the often underestimated nutritional management. The role of multidisciplinary teams and of the active involvement of patients and their families is stressed. The creation of a coherent cystic fibrosis health care system (both in paediatrics and internal medicine) on a regional and nation-wide scale will undoubtedly play an important role in successful treatment.