[Doyne-type honeycombed macular degeneration]

The case of a 52-year-old patient, who presents since his youth round areas, white to yellow, sometimes confluent, having an aspect of mosaic, in the macular, papillary and intermaculopapillary regions, is examined. In the macular region of the left eye a red macular area has an aspect of pseudohole. The visual acuity is good, with image distortion at proximity. Central little scotomas can be seen, the computerized perimetry also reveals the diminish of the visual capacity at 802 (RE) and 785 (LE). The adaptometry is slightly diminished, there is also a unsystematic dyschromatopsia at pseudo-iso-chromatic tables. Angiographically there is a hyperfluorescence with overlaps on the ophthalmoscopical yellow-white areas. The lesions are interpreted as Doyne degenerescence, due to mucopolyzaharide deposits in the cuticular layer of Bruch membrane. The particularity of the case consist of a good conservation of visual function, compared to ophthalmoscopic lesions.