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Adamantinoma of the appendicular skeleton in children
1Presbyterian Health Care Services, Albuquerque, New Mexico, USA.
International Orthopaedics
|January 1, 1994
Insights
Adamantinoma, a rare bone tumor, affects children and adults similarly, with a 20% mortality rate. The optimal treatment for pediatric patients involves wide excision and bone grafting.
Area of Science:
- Orthopedic Oncology
- Pediatric Oncology
- Skeletal Tumors
Background:
- Adamantinoma is a rare, primary bone tumor of epithelial origin.
- Reviewing global literature on adamantinoma cases provides insights into its characteristics.
Observation:
- A review of 260 worldwide adamantinoma cases was conducted.
- Sixty pediatric cases (≤16 years) were analyzed, showing similarities to adult presentations.
Findings:
- The mortality rate for adamantinoma is consistently 20% across both pediatric and adult populations.
- Wide surgical excision combined with bone grafting is identified as the preferred treatment modality for pediatric adamantinoma.
Implications:
- This highlights the need for aggressive surgical management in young adamantinoma patients.
- Effective treatment strategies can potentially improve outcomes for this rare skeletal malignancy.
Abstract:
The 260 cases of adamantinoma described in the world literature have been reviewed. Case histories of 60 patients up to the age of 16 years mirror those of adults. The mortality rate is 20% in children and adults. Wide excision with bone grafting is the ideal treatment for patients under 16 years.