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Dyskeratosis congenita
1Division of Pediatric Hematology/Oncology, University of Medicine and Dentistry, New Jersey-Robert Wood Johnson Medical School, New Brunswick, USA.
Dermatologic Clinics
|January 1, 1995
Abstract:
Dyskeratosis congenita is a rare genodermatosis. Malignant deterioration and hematologic complications are well-described features of this syndrome. Correct recognition is essential for proper management. A review of diagnostic considerations and treatment guidelines is presented.