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Orbital lymphangioma with intracranial extension
J L Zucker1, M Assaad, M R Levine
1Division of Ophthalmology, Northeastern Ohio Universities College of Medicine, Rootstown, USA.
Ophthalmic Plastic and Reconstructive Surgery
|March 1, 1995
Summary
This case study details an orbital lymphangioma in a 14-year-old boy that spread intracranially. The benign tumor caused vision loss and recurrent infections, highlighting its aggressive progression.
Area of Science:
- Ophthalmology
- Neurology
- Pediatric Oncology
Background:
- Orbital lymphangiomas are benign vascular tumors that can present in childhood.
- Congenital orbital lymphangioma can lead to significant functional and cosmetic issues.
- Intracranial extension of orbital lymphangioma is rare.
Observation:
- A 14-year-old boy with a history of congenital orbital lymphangioma and hydrocephalus presented with vision loss and disfigurement.
- The patient experienced 12 episodes of severe periorbital and orbital cellulitis.
- Imaging revealed tumor invasion beyond the orbit into the middle cranial fossa.
Findings:
- Biopsy confirmed orbital lymphangioma with contiguous intracranial spread.
- The tumor extended through orbital fissures and paranasal sinuses extradurally.
- Progressive posterior extension intracranially was documented in this unique case.
Implications:
- This case underscores the potential for aggressive intracranial progression of orbital lymphangioma.
- Recurrent orbital cellulitis may be a complication of advanced orbital lymphangioma.
- Management strategies for orbital lymphangioma require consideration of potential intracranial involvement.