[The amyotrophic lateral sclerosis syndrome--frontal-type dementia]

The article presents analysis of clinical case of and review of literature on "ALS-dementia complex", a combination of ALS syndrome and dementia predominantly of frontal lobe type. The review of literature contains discussion on the problem of lobe dementia, analysis of relation of ALS-dementia syndrome and the following diseases: Alzheimer, Pick, Creutzfeldt-Jakob, Lewy bodies, Charcot (classic type), multisystem degeneration. Polymorphism of ALS-dementia complex and the possibilities of its differential diagnosis are considered.