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Foot deformities in arthrogryposis multiplex congenita
1Department of Surgery and Orthopedics, Children's Hospital, University Central Hospital, Helsinki, Finland.
Journal of Pediatric Orthopedics
|November 1, 1994
Summary
Foot deformities, particularly talipes equinovarus, are prevalent in arthrogryposis multiplex congenita. Surgical interventions are primary, but recurrences are common, necessitating extensive initial treatment and addressing associated knee/hip deformities.
Area of Science:
- Pediatric Orthopedics
- Congenital Disorders
Background:
- Foot deformities are a frequent manifestation of arthrogryposis multiplex congenita.
- In a cohort of 52 patients, 43 presented with foot deformities, predominantly bilateral talipes equinovarus.
Purpose of the Study:
- To analyze the treatment strategies and outcomes for foot deformities in arthrogryposis multiplex congenita.
- To evaluate the effectiveness of different surgical approaches and identify factors influencing recurrence.
Main Methods:
- Retrospective review of 52 patients diagnosed with arthrogryposis multiplex congenita and foot deformities.
- Analysis of surgical procedures, including Brockmann's procedure and posteromedial/posteromedioplantar release.
- Assessment of recurrence rates and the impact of associated knee and hip deformities.
Main Results:
- Talipes equinovarus was the most common deformity (72 feet).
- Operative treatment was the primary approach for all 52 patients.
- Recurrences were frequent, with 36 procedures performed on 15 feet for recurrent talipes equinovarus.
- Associated knee and hip deformities, especially knee issues, complicated outcomes.
Conclusions:
- Primary surgical treatment for arthrogryposis multiplex congenita foot deformities must be comprehensive to prevent recurrence.
- Addressing concurrent knee and hip deformities is crucial for successful long-term management.
- Talectomy and bone decancellation show promise in managing recurrent deformities.