[Protruding dermatofibrosarcoma. An unusual cutaneous tumor]

Local reoccurrence of protuberant dermatofibrosarcoma was seen in a female patient 3 years after exeresis. We reviewed the data in the literature on the physical examination, outcome, histology and therapeutic approach. The Darier and Ferrand dermatofibroma is a very unusual skin tumour which develops in the dermal layer. Diagnosis can only be confirmed by histologicaal examination of the specimen. Wide surgical exeresis is required to avoid local relapse. Despite the high risk of reoccurrence, the prognosis is excellent.