[Laryngeal changes in mucoviscidosis]
Insights
Cystic fibrosis, a hereditary disease, rarely presents with laryngological symptoms. This study observed five children with cystic fibrosis, three with nasal polyps and two with recurrent parotid gland infections.
Area of Science:
- Otolaryngology
- Pediatrics
- Genetics
Background:
- Mucoviscidosis, also known as cystic fibrosis, is a congenital, hereditary disorder affecting exocrine glands.
- Laryngological manifestations of cystic fibrosis are infrequently encountered in clinical practice.
Observation:
- This study examined five pediatric patients diagnosed with cystic fibrosis.
- Three patients underwent surgical intervention for nasal and paranasal sinus polyps.
- Two patients were monitored for recurrent parotid gland infections.
Findings:
- The case series highlights the occurrence of otolaryngological symptoms in pediatric cystic fibrosis patients.
- Nasal polyposis and parotid gland infections represent potential clinical presentations.
Implications:
- Increased awareness of these laryngological symptoms may aid in earlier diagnosis and management of cystic fibrosis.
- Further research is warranted to elucidate the specific mechanisms linking cystic fibrosis to these otolaryngological issues.
Abstract:
Mucoviscidosis (cystic fibrosis) is congenital and hereditary disease of excretion glands expose in infancy and school age. In clinical practice we very rare meet cases of mucoviscidosis with laryngological symptoms. Our study include 5 children examined in Children Hospital in Cracow. Three children were operated due to polyps in nose and paranasal sinuses. Two children are observed due to return infections in the parotid glands.
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