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[Aortic root replacement in twin Marfan patients]
1Department of Cardiovascular Surgery, Hokkaido Ohno Hospital, Sapporo, Japan.
Abstract:
We have performed aortic root replacement in twin Marfan patients. They were male and aged 33 years at the times of the operations. One had pneumonia but the other had no complaints. Echocardiography showed geometries typical of annuloaortic ectasia (aortic diameters of 6.4 and 6.8 cm) and a moderate degree of aortic insufficiency. Aortic roots were replaced utilizing composite valve graft and the coronary orifices were reimplanted with Carrel's patch technique. The operations were carried out at almost the same time. The patients had a satisfactory postoperative course. Because of the potential for late dissection or aneurysm in other areas of the aorta, they should have regular follow-up examinations by MRI and CT indefinitely.
Insights
Aortic root replacement using composite valve grafts was successfully performed in 33-year-old Marfan syndrome twins. Long-term cardiovascular surveillance is recommended for these patients.
Area of Science:
- Cardiovascular Surgery
- Genetics
- Marfan Syndrome
Background:
- Marfan syndrome is a genetic disorder affecting connective tissue, often leading to aortic root dilation and dissection.
- Aortic root ectasia and insufficiency pose significant risks, necessitating surgical intervention.
Observation:
- Two 33-year-old male twins with Marfan syndrome presented with annuloaortic ectasia (aortic diameters 6.4 and 6.8 cm) and moderate aortic insufficiency.
- One twin experienced preoperative pneumonia, while the other was asymptomatic.
Findings:
- Aortic root replacement was performed using composite valve grafts with Carrel's patch technique for coronary reimplantation.
- Both patients had a satisfactory postoperative recovery.
Implications:
- Composite valve grafting is an effective surgical option for Marfan syndrome patients with aortic root pathology.
- Lifelong surveillance with MRI and CT is crucial to monitor for potential late aortic dissections or aneurysms in other aortic segments.