[One and one half ventricle repair for pure pulmonary atresia--a case report]

One and one half ventricle repair consisting of the Glenn operation and the right ventricular outflow tract reconstruction was performed in a 4-year-old boy. The diagnosis of this patient was pure pulmonary atresia. He had undergone Brock's operation, Blalock-Taussig shunt and a central shunt at neonatal period. At the time of one and one half ventricle repair, the connection between the superior vena cava and the right atrium was left open. Although the RVEDV was 34.3% of normal, the topology of the right ventricle was tripartite. At three months after one and one half ventricle repair, RVEDV increased up to 52.7% of normal. This data suggests that a further definitive surgery, i.e., complete biventricular repair could be applicable in the future.