Right ventricular hypoplasia: outcome after conservative perinatal management

Isolated right ventricular hypoplasia is a rare congenital cardiac anomaly. A case described in which prenatal diagnosis was made by echocardiography. Conservative perinatal management produced a favourable short-term outcome without compromising the definitive surgical intervention later. The decisions were based on principles used in the treatment of pulmonary atresia with intact interventricular septum.