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Emergency operation for thoracic aortic aneurysm caused by the Ehlers-Danlos syndrome
K Hamano1, Y Minami, Y Fujimura
1First Department of Surgery, Yamaguchi University School of Medicine, Japan.
The Annals of Thoracic Surgery
|October 1, 1994
Abstract:
Two patients were treated emergently for impending ruptured thoracic aortic aneurysms caused by type IV Ehlers-Danlos syndrome. One patient had typical physical evidence of type IV Ehlers-Danlos syndrome. The other patient had a normal phenotype. Type IV Ehlers-Danlos syndrome was diagnosed by electrophoresis of the collagen extracted from the skin. The clinician must be aware of the variations in presentation of type IV Ehlers-Danlos syndrome.