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[Infantile scleroderma. Apropos of 11 cases]
J Goldenberg1, A Pinto-Pessoa, M Odete-Hilario
1Escola Paulista de Medicina, Disciplina de Reumatologia, São Paulo, Brésil.
Revue Du Rhumatisme (Ed. Francaise : 1993)
|February 1, 1993
Insights
Scleroderma is rare in pediatric patients, with only 84 cases previously reported. A new study of 11 pediatric scleroderma cases shows a good prognosis with no deaths or significant organ damage.
Area of Science:
- Pediatric rheumatology
- Dermatology
- Autoimmune diseases
Context:
- Scleroderma is an uncommon autoimmune condition affecting connective tissues.
- Limited data exists on pediatric scleroderma cases, with only 84 reported globally.
- This study examines a new cohort of 11 pediatric patients.
Purpose:
- To describe the clinical features and disease course of scleroderma in children and adolescents.
- To assess the prognosis and outcomes of pediatric scleroderma.
- To contribute to the understanding of this rare condition in a young population.
Summary:
- Eleven new cases of childhood scleroderma were analyzed.
- The study details the clinical presentation and progression of the disease.
- Key findings indicate a favorable prognosis, with no mortality or significant visceral involvement.
Impact:
- Provides valuable insights into the clinical spectrum of pediatric scleroderma.
- Highlights the generally good prognosis for children diagnosed with this condition.
- Informs clinical management and patient counseling for pediatric scleroderma.
Abstract:
Scleroderma is uncommon in children and adolescents. Eighty-four cases have been reported. With reference to a new series of 11 cases, the clinical features and course of the disease are described. Prognosis was good. There have been no deaths and none of the patients have significant visceral organ damage.