[Combination of Cantrell pentalogy and amniotic band syndrome: a case report]

A case is reported of sonographic diagnosis of ADAM-complex (amniotic band syndrome) in combination with Cantrell-syndrome in the 19th gestational week. The ultrasonic investigation also showed a large defect in the fetal skull with encepholocele as well as a marked defect of the abdominal wall and chest with dislocation of the intestines, liver, and heart. The pregnancy was interrupted because of the severe fetal malformations. Aetiology and pathogenesis of such rare abnormalities and possible correlations between ADAM-syndrome and Cantrell-syndrome are discussed with reference to the literature.