Related Experiment Videos
Presenile-onset cerebral adrenoleukodystrophy presenting as Balint's syndrome and dementia
1First Department of Internal Medicine, Kumamoto University School of Medicine, Japan.
Neurology
|June 1, 1993
Abstract:
We describe a patient with presenile-onset cerebral adrenoleukodystrophy presenting as Balint's syndrome and dementia. There were demyelinating MRI changes in the parieto-occipital white matter bilaterally, including the splenium of the corpus callosum. Therapeutic trials using 1-deamino-(8-D-arginine)-vasopressin, very long-chain fatty acid-free diet, and gamma-globulin were of no benefit.