[Erdheim-Chester disease. A rare etiology of retrobulbar tumor]

The authors report the case of a 47 year old man who presented with bilateral retro-ocular tumor and an inflammatory syndrome as the first sign of his disease. Later on, the illness became polyvisceral and biopsies of retro-ocular and retro-peritoneal tissues revealed the diagnosis of Erdheim-Chester disease. The patient died a few months later.