[EEG in diagnosis of other disease pictures than epilepsy]

Electroencephalography plays a very important role in the diagnosis and course monitoring of epilepsy. The EEG is also able to give decisive clues in diseases other than epilepsy. It is important to know these specific EEG patterns which may assume a key role in the diagnosis of rare neuropediatric diseases. Familiarity with such specific patterns will allow to select only specific investigations for diagnostic confirmation. We report six guiding EEG patterns and the associated disorders: 1. Re-build up phenomena for Moyamoya syndrome. 2. High amplitude alpha-beta activity for lissencephaly type I. 3. Positive spikes during low frequency photostimulation for late infantile neuronal ceroid lipofuscinosis. 4. Periodic high amplitude discharges for subacute sclerosing panencephalitis (SSPE). 5. Burst suppression pattern in non-asphyctic mature newborns for Ohtahara syndrome, non ketotic hyperglycinemia or molybden cofactor deficiency. 6. High amplitude 3-4 HZ activity with small spikes for Angelman syndrome.