Ameloblastic dentinosarcoma- a case report

A rare case of ameloblastic dentinosarcoma is reported. The literature regarding ameloblastic fibro- and odontosarcomas is reviewed. There have been 16 reported cases of ameloblastic fibrosarcoma and another six cases (one uncertain) of ameloblastic fibrosarcoma which showed induction of dentin or enamel and which therefore according to the WHO Classification should be separately classified as ameloblastic odontosarcomas. Our case showed no enamel and therefore is better called ameloblastic dentinosarcoma. Ameloblastic sarcomas of the jaws are of low grade malignancy, do not often metastasize, and if treated by radical resection have a good prognosis.