Related Experiment Videos
Sudden sensorineural hearing loss in haemoglobin SC disease
M E Tavin1, J S Rubin, F J Camacho
1Department of Otorhinolaryngology, Montefiore Medical Center, Bronx, NY.
The Journal of Laryngology and Otology
|September 1, 1993
Summary
Sudden sensorineural hearing loss is rarely associated with hemoglobin SC disease. Partial exchange transfusions may stabilize and improve hearing in affected patients, warranting further investigation.
Area of Science:
- Hematology
- Otolaryngology
- Genetics
Background:
- Sudden sensorineural hearing loss (SSNHL) is an otologic emergency.
- Hemoglobin SC (HbSC) disease is a rare hemoglobinopathy.
- The association between SSNHL and HbSC disease is exceptionally rare, with limited literature.
Observation:
- A rare case of SSNHL occurred in a patient with hemoglobin SC disease.
- This is only the second reported instance in medical literature.
Findings:
- Partial exchange transfusions were administered to reduce blood viscosity and enhance flow.
- Hearing stabilized post-transfusion and subsequently showed gradual improvement.
Implications:
- Exchange transfusions may offer a potential therapeutic strategy for SSNHL in hemoglobin SC disease.
- The findings suggest a theoretically sound, albeit circumstantial, benefit requiring further research.