Related Experiment Videos
Total anomalous pulmonary venous connection. Results of a small consecutive series
T Le Minh1, H Demanet, P Viart
1Department of Cardiac Surgery, Hôpital Universitaire Brugmann, Brussels, Belgium.
Insights
Early surgical repair of total anomalous pulmonary venous connection (TAPVC) in infants is safe and effective. This study shows no operative deaths and good medium-term outcomes for infants undergoing TAPVC correction.
Area of Science:
- Pediatric Cardiac Surgery
- Congenital Heart Defects
- Cardiovascular Physiology
Background:
- Total anomalous pulmonary venous connection (TAPVC) is a critical congenital heart defect.
- Surgical outcomes for TAPVC historically varied, necessitating review of early repair strategies.
Purpose of the Study:
- To review the surgical experience and outcomes of infants with TAPVC treated between 1987 and 1991.
- To evaluate the feasibility and medium-term results of early surgical intervention for TAPVC.
Main Methods:
- Retrospective review of 13 infants with TAPVC undergoing surgical repair.
- Analysis of patient demographics, TAPVC subtypes, surgical techniques (profound hypothermia with circulatory arrest vs. continuous hypothermic bypass), and follow-up data.
Main Results:
- No operative deaths occurred in 13 infants.
- All patients were asymptomatic at a mean follow-up of 40 months, with one reoperation.
- Growth percentiles were <5% for height in 20% and weight in 30% of patients.
Conclusions:
- Early surgical repair of TAPVC in infants can be performed with low morbidity.
- Favorable medium-term outcomes suggest that prompt intervention is beneficial for infants with TAPVC.
Abstract:
The surgical experience in 13 infants with total anomalous pulmonary venous connection (TAPVC) between 1987 and 1991 is reviewed. The age vary from 2 days to 35 months with a weight at intervention from 2.130 kg to 5.400 kg. The types of TAPVC were supracardiac in 4 patients, cardiac in 4, and infracardiac in 5. Seven patients (54%) were operated on in emergency. Cardiopulmonary bypass consisted of profound hypothermia and total circulatory arrest in 8 patients (60%) and continuous hypothermic bypass with low flow for the remaining 5 patients (40%). There was no operative death. The follow-up ranges from 21 to 58 months, mean 40 months. There was one reoperation. All the patients were asymptomatic and the height growth percentile is less than 5% in 20%, and the weight growth percentile is less than 5% in 30%. The early repair of infants born with TAPVC can be done with low morbidity with a good prospect on medium term follow-up.