Right coronary artery cirsoid with fistulous connection to the coronary sinus

F Tomai1, L Sommariva, F Nudi

  • 1Servizio Speciale di Diagnosi e Cura di Emodinamica, Università Tor Vergata, European Hospital, Rome, Italy.

Insights

This case report details a rare anomaly where a right coronary artery abnormally connected to the coronary sinus. Cardiac catheterization confirmed the diagnosis and quantified the left-to-right shunt, crucial for surgical planning.

Area of Science:

  • Cardiology
  • Medical Imaging
  • Vascular Surgery

Background:

  • Right atrial myxoma is a rare cardiac tumor.
  • Anomalous coronary artery origins can lead to complex cardiovascular conditions.
  • Coronary artery fistulas require accurate diagnosis and management.

Observation:

  • A 61-year-old woman presented with suspected right atrial myxoma.
  • Transesophageal echocardiography suggested an anomalous right coronary artery with a fistulous connection to the coronary sinus.
  • Cardiac catheterization revealed an oxygen step-up in the right atrium, indicating a significant left-to-right shunt.

Findings:

  • Aortic root angiography demonstrated a large, calcified right coronary artery cirsoid draining into a dilated coronary sinus.
  • The findings confirmed a rare coronary artery anomaly, not a right atrial myxoma.
  • A left-to-right shunt of 1.3:1.0 was quantified via cardiac catheterization.

Implications:

  • Cardiac catheterization is essential for diagnosing and quantifying shunts in anomalous coronary artery fistulas.
  • Accurate shunt quantification guides the decision for surgical intervention.
  • This case highlights the importance of comprehensive diagnostic evaluation for complex congenital heart anomalies.

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