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Systolic and diastolic function in tricuspid valve atresia before the Fontan operation

G G Sandor1, M W Patterson, J G LeBlanc

  • 1Department of Paediatrics and Cardiovascular Surgery, University of British Columbia, British Columbia's Children's Hospital, Vancouver, Canada.

Insights

Young patients with tricuspid atresia show impaired systolic function despite normal diastolic function. This study highlights abnormalities in both load-dependent and independent systolic indexes before surgery.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Tricuspid atresia is a complex congenital heart defect requiring early intervention.
  • Understanding preoperative cardiac function is crucial for surgical planning and patient outcomes.

Purpose of the Study:

  • To assess systolic and diastolic cardiac function in pediatric patients with classic tricuspid atresia.
  • To compare cardiac function parameters between patients and control subjects.

Main Methods:

  • Cardiac catheterization was performed on 6 patients with tricuspid atresia and systemic-to-pulmonary shunts.
  • Left ventricular volumes, mass, pressures, and myocardial stiffness were measured.
  • Load-dependent and independent indexes of systolic function were analyzed.

Main Results:

  • Patients had significantly larger left ventricular volumes and masses, and higher end-systolic and peak systolic stress.
  • Rate-corrected mean velocity of fiber shortening was lower in patients.
  • Diastolic function and myocardial stiffness were found to be normal.

Conclusions:

  • Preoperative tricuspid atresia is associated with abnormal systolic function, including impaired contractility and altered load-dependent indexes.
  • Diastolic function remains normal in these young patients.
  • Findings suggest significant ventricular remodeling and altered mechanics prior to surgical correction.

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