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Sternal cleft associated with vascular anomalies and micrognathia
1Clinic for Cardiovascular Surgery, University Hospital Zurich, Switzerland.
The Annals of Thoracic Surgery
|July 1, 1993
Summary
Sternal clefts rarely occur with craniofacial vascular defects. This case highlights the need to screen for internal vascular anomalies in patients with sternal clefts.
Area of Science:
- Cardiovascular Surgery
- Medical Genetics
- Pediatric Cardiology
Background:
- Sternal clefts are rare congenital anomalies.
- Craniofacial vascular defects, such as hemangiomata, can be associated with sternal anomalies.
- Complex congenital conditions require multidisciplinary management.
Observation:
- A 45-year-old woman presented with a sternal cleft and multiple craniofacial and brain hemangiomata.
- Associated anomalies included an aortic arch aneurysm, anomalous coronary artery origin, left superior vena cava, micrognathia, supraumbilical midline raphe, and a cervical cyst.
- Surgical intervention involved aortic arch and innominate artery replacement under deep hypothermia and circulatory arrest.
Findings:
- This case demonstrates a rare association between sternal cleft and extensive vascular anomalies.
- The surgical repair of the aortic arch aneurysm was successfully performed.
- The patient's complex condition underscores the importance of thorough diagnostic evaluation.
Implications:
- Sternal clefts should prompt a search for associated internal vascular anomalies.
- Early detection and management of these complex conditions are crucial for patient outcomes.
- This case contributes to understanding the spectrum of sternal and vascular malformations.