Related Experiment Videos
Congenital histiocytosis X
1Department of Radiology, Loyola University Medical Center, Maywood, Illinois 60153.
Pediatric Radiology
|January 1, 1993
Summary
Congenital histiocytosis X, a rare and fatal neonatal disease, requires consideration in infants with skin lesions. This case highlights respiratory failure from diffuse lung infiltration by histiocytic cells.
Area of Science:
- Neonatal Medicine
- Dermatology
- Pathology
Background:
- Congenital histiocytosis X (Letterer-Siwe disease) is a rare condition with high intrauterine and neonatal mortality.
- Early diagnosis is crucial for neonates presenting with characteristic vesiculated crusting skin lesions.