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Neurocutaneous melanosis associated with inferior vermian hypoplasia: MR findings
1Department of Diagnostic Radiology, Chang Gung Memorial Hospital, Taipei, Taiwan, R.O.C.
Objective:
We describe the MR findings of two cases of neurocutaneous melanosis (NCM) associated with inferior vermian hypoplasia (IVH).
Materials And Methods:
Two cases of NCM associated with IVH are presented. Both patients had congenital giant hairy nevi and multiple satellite lesions.
Results:
Magnetic resonance imaging revealed IVH as well as hyperintensities in the pons and the cerebellar leptomeninges on T1-weighted images. The hyperintensities may be ascribed to the T1-shortening effect of melanin. A right parietal tumor in one patient and unilateral ventriculomegaly in another patient were also depicted.
Conclusions:
Magnetic resonance demonstration of the T1-shortening leptomeningeal infiltrations adds weight to the diagnosis of NCM. The implication of the concurrence of NCM and IVH is discussed.