An unusual presentation of pigmented villonodular synovitis

A case of multiple joint and tendon involvement by PVS seems not to have been preciously reported. In a 7-year-old girl there were other organ system problems usually not seen with PVS, and the entire complex may represent a more generalized disease process. The diffuse form of the disease was refractory to multiple attempts at surgical excision. The similarities between PVS and synovial hemangioma suggest that it is important to establish the diagnosis after the first operation.