Ganglioside metabolism--topology and regulation

A direct gene transfer strategy via brain internal capsule reverses the biochemical defect in Tay-Sachs disease.

Human molecular genetics·2005

Acid sphingomyelinase deficiency. Phenotype variability with prevalence of intermediate phenotype in a series of twenty-five Czech and Slovak patients. A multi-approach study.

Journal of inherited metabolic disease·2005

Correlation between enzyme activity and substrate storage in a cell culture model system for Gaucher disease.

Journal of inherited metabolic disease·2005

Long endogenous dsRNAs can induce complete gene silencing in mammalian cells and primary cultures.

Oligonucleotides·2004

Toxicity of glucosylsphingosine (glucopsychosine) to cultured neuronal cells: a model system for assessing neuronal damage in Gaucher disease type 2 and 3.

Neurobiology of disease·2003

Reduced rates of axonal and dendritic growth in embryonic hippocampal neurones cultured from a mouse model of Sandhoff disease.

Neuropathology and applied neurobiology·2003

Sphingolipids with inositolphosphate-containing head groups.

Advances in lipid research·1993

Neutral sphingomyelinase.

Advances in lipid research·1993

Ceramide: a novel second messenger.

Advances in lipid research·1993

Why is the chloroplast redox regulatory machinery so complex?

Molecular plant·2026

Parallel intracellular redox and extracellular respiration sensing for quantitative oxidative stress profiling.

Biosensors & bioelectronics·2026

Nuclear receptor-mediated control of bile composition: implications for gallstone formation.

Irish journal of medical science·2026

Liver organoids: modelling complexity in homeostasis and disease.

FEBS letters·2026

Serine: From Metabolic Intermediate to Signaling Entity.

Biochemistry·2026

Proton flows, proton gradients and subcellular architecture in biological energy conversion.

Physical biology·2026

Related Experiment Videos

Ganglioside metabolism--topology and regulation

Related Concept Videos

A direct gene transfer strategy via brain internal capsule reverses the biochemical defect in Tay-Sachs disease.

Acid sphingomyelinase deficiency. Phenotype variability with prevalence of intermediate phenotype in a series of twenty-five Czech and Slovak patients. A multi-approach study.

Correlation between enzyme activity and substrate storage in a cell culture model system for Gaucher disease.

Long endogenous dsRNAs can induce complete gene silencing in mammalian cells and primary cultures.

Toxicity of glucosylsphingosine (glucopsychosine) to cultured neuronal cells: a model system for assessing neuronal damage in Gaucher disease type 2 and 3.

Reduced rates of axonal and dendritic growth in embryonic hippocampal neurones cultured from a mouse model of Sandhoff disease.

Sphingolipids with inositolphosphate-containing head groups.

Neutral sphingomyelinase.

Ceramide: a novel second messenger.

Why is the chloroplast redox regulatory machinery so complex?

Parallel intracellular redox and extracellular respiration sensing for quantitative oxidative stress profiling.

Nuclear receptor-mediated control of bile composition: implications for gallstone formation.

Liver organoids: modelling complexity in homeostasis and disease.

Serine: From Metabolic Intermediate to Signaling Entity.

Proton flows, proton gradients and subcellular architecture in biological energy conversion.

Related Experiment Videos

Ganglioside metabolism--topology and regulation

Related Concept Videos

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