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Recurrent meningococcal infections in a patient with congenital C5 deficiency

A Bols1, J Janssens, W Peetermans

  • 1Department of General Internal Medicine, University Hospitals, K. U. Leuven, Belgium.

Acta Clinica Belgica
|January 1, 1993
PubMed

Insights

A rare C5 complement deficiency caused recurrent meningococcal disease in a 27-year-old man. Early antibiotics and vaccination are recommended for individuals with this rare immune deficiency.

Area of Science:

  • Immunology
  • Infectious Diseases
  • Genetics

Background:

  • Recurrent Neisseria infections can indicate underlying immune system dysfunction.
  • Deficiencies in late complement components impair the body's ability to fight certain bacterial infections.

Observation:

  • A 27-year-old male presented with recurrent meningococcal disease.
  • Congenital deficiency of the C5 complement component was identified as the cause.

Findings:

  • C5 deficiency leads to a lack of serum bactericidal activity against Neisseria meningitidis.
  • This deficiency explains the increased incidence and altered disease course of Neisseria infections.

Implications:

  • Early antibiotic intervention is crucial for patients with C5 deficiency experiencing meningococcal disease.
  • Vaccination with capsular polysaccharide meningococcal vaccines (serogroups A, C, Y, W-135) is recommended for prevention.

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