[Palliative management of left atrioventricular valve atresia with normal aortic valve]

We present three cases of the left atrioventricular valve atresia (LAVVA) with normal aortic valve. All cases showed [S,D,D] and had concordant AV connection. First case had two functional ventricles with multiple VSD and ventriculo-arterial connection was normal. Interatrial communication was maintained through ASD and the infant underwent pulmonary arterial banding (PAB). Four years later, the patient underwent Blalock-Hanlon (B-H) procedure for an inadequate ASD. Second case showed the univentricular heart of right ventricle with double outlet. In this case, PFO was restrictive and the infant underwent B-H procedure. Ten days after initial palliation, patient underwent PAB. Third case showed the univentricular heart of left ventricle and transposed great arteries. This patient had also the coarctation of the aorta. B-H procedure, PAB and subclavian flap aortoplasty were performed simultaneously by bilateral thoracotomy. All patients have done well, with normal growth and development at the time of their last outpatient evaluation at 10 year, 9 months and 9 months after surgery respectively.