Epidermolysis bullosa acquisita (EBA) with nonclassical distribution of eruptions

The skin lesions in epidermolysis bullosa acquisita (EBA), a mechanobullous disease, often show acral distribution. Recently, we experienced a case of EBA in which most of the skin lesions were located on the trunk. We reviewed the distribution of the skin eruptions in 58 reported cases of EBA. Although the extensor surfaces of the extremities are the most common site, there were some cases with non-acral distribution. These "nonclassical" cases should also be considered in the clinical diagnosis of EBA and other bullous diseases.