Double aortic arch causing tracheoesophageal compression

M T Han1, D G Hall, A Manché

  • 1Department of Cardiovascular Surgery, Children's Hospital and Medical Center, Seattle, Washington 98105.

Insights

Surgical repair of double aortic arch in 17 pediatric patients effectively resolved respiratory and swallowing issues. Early intervention before 24 months improved outcomes, with no mortality and complete symptom resolution in all cases.

Area of Science:

  • Cardiovascular Surgery
  • Pediatric Thoracic Surgery
  • Congenital Heart Disease

Background:

  • Double aortic arch is a rare congenital vascular anomaly causing extrinsic compression of the trachea and esophagus.
  • Symptoms often manifest in infancy, including respiratory distress and feeding difficulties.

Purpose of the Study:

  • To review the surgical management and outcomes of patients with double aortic arch treated at a single institution.
  • To evaluate the efficacy of surgical intervention in alleviating symptoms associated with this condition.

Main Methods:

  • Retrospective review of 17 patients surgically treated for double aortic arch since 1972.
  • Diagnostic modalities included barium swallow and bronchoscopy to assess esophageal and tracheal compression.
  • Surgical techniques involved division of the dominant arch, resection of Kommerell's diverticulum when present, and vascular suspension for tracheal/esophageal release.

Main Results:

  • All 17 patients underwent successful surgical correction, with 16 having the anterior arch divided and one the posterior arch.
  • 11 patients required surgery before 12 months of age, and 16 before 24 months.
  • Four patients had Kommerell's diverticulum resected; 13 required vascular suspension.
  • Complete symptomatic improvement was achieved in all patients, with no mortality.
  • Four patients experienced residual symptoms potentially due to tracheomalacia.

Conclusions:

  • Surgical correction of double aortic arch is highly effective in treating pediatric patients with symptomatic vascular rings.
  • Early surgical intervention is crucial for optimal outcomes.
  • While generally curative, residual symptoms may occur, possibly related to associated tracheomalacia.

Related Concept Videos

The Arch of Aorta01:10

The Arch of Aorta

The coronary arteries, originating from the ascending aorta, bifurcate from two sinuses located within the ascending aorta. Positioned just above the aortic semilunar valve, these sinuses house essential aortic baroreceptors and chemoreceptors, crucial for maintaining cardiac function. The left coronary artery and the right coronary artery branch off from the left posterior and anterior aortic sinuses, respectively.
Encircling the heart, the coronary arteries form a ring-like structure before...
Thoracic Aorta01:15

Thoracic Aorta

The thoracic section of the aorta begins at the T5 vertebra and extends to the T12 level at the diaphragm, initially progressing through the mediastinum to the left of the spinal column. Throughout its course in the thoracic segment, the thoracic aorta emits various offshoots known collectively as visceral and parietal branches. The branches that predominantly supply blood to visceral organs are termed visceral branches and include bronchial, pericardial, esophageal, and mediastinal arteries,...
Trachea01:22

Trachea

The trachea, commonly known as the windpipe, is a vital part of the human respiratory system. It serves as a passageway for air to travel between the larynx and the bronchi, allowing oxygen to reach the lungs. Let's explore its anatomical features, dimensions, layers of the tracheal wall, associated muscles, and the functions of its parts.
Anatomical Features:
Location: About half of the trachea is situated in the neck, anterior to the esophagus, and extends from the larynx (at the level of the...
Oxygen Delivering System II: Venturi Mask and Transtracheal Oxygen01:16

Oxygen Delivering System II: Venturi Mask and Transtracheal Oxygen

Oxygen therapy is a pivotal aspect of medical care, particularly for patients with respiratory ailments. Two prominent oxygen-delivering systems include the Venturi mask and the transtracheal oxygen catheter.
Venturi Mask
The Venturi mask, named after the Venturi effect, is designed to deliver precise oxygen concentrations. It consists of a large tube with an oxygen inlet that narrows down, causing a pressure drop that pulls air in through adjustable side ports. The mask is a lightweight,...
Aortic Regurgitation II: Clinical Features and Diagnostic Tests01:22

Aortic Regurgitation II: Clinical Features and Diagnostic Tests

Aortic valve regurgitation (AR) occurs when the aortic valve fails to close properly, allowing blood to flow backward from the aorta into the left ventricle. This backflow can result in two distinct clinical presentations: acute and chronic AR, each characterized by its own set of symptoms and physical findings.Acute Aortic RegurgitationAcute AR presents with a sudden onset of severe symptoms. Patients typically experience profound dyspnea (shortness of breath), chest pain, and signs of left...
Aneurysm II: Clinical Manifestations and Diagnostic Studies01:21

Aneurysm II: Clinical Manifestations and Diagnostic Studies

Thoracic, aortic arch and abdominal aneurysms are significant vascular conditions that can present with various clinical manifestations and lead to serious complications. Understanding these manifestations and the appropriate diagnostic studies is essential for effective management and treatment.Thoracic Aortic AneurysmsThoracic aortic aneurysms often remain asymptomatic until they reach a size that impinges on adjacent structures. They typically cause deep, diffuse chest pain that radiates to...