Related Experiment Videos
Multifocal pigmented villonodular synovitis in a child. A case report
R M Kay1, J J Eckardt, J M Mirra
1Department of Orthopaedic Surgery, UCLA School of Medicine 90095-6902, USA.
Clinical Orthopaedics and Related Research
|January 1, 1996
Summary
Pigmented villonodular synovitis (PVNS) typically affects one site. This report details an unusual pediatric case of multifocal PVNS, impacting multiple joints and tendons across both upper and lower extremities.
Area of Science:
- Orthopedics
- Pediatric Rheumatology
- Musculoskeletal Oncology
Background:
- Pigmented villonodular synovitis (PVNS) is a rare, benign neoplastic proliferation of the synovium.
- PVNS commonly presents as a monoarticular disease, predominantly affecting the knee.
Observation:
- This case report describes an unusual presentation of PVNS in an otherwise healthy child.
- The patient exhibited multifocal involvement, affecting multiple joints and tendon sheaths.
- Asymmetric disease distribution was noted across both upper and lower extremities, including the pes anserine tendons.
Findings:
- The pediatric patient presented with widespread, rather than localized, pigmented villonodular synovitis.
- Multisite involvement included joints and tendon structures in both the upper and lower limbs.
- Pes anserine tendon involvement represents a rare manifestation in pediatric PVNS.
Implications:
- This case highlights the potential for multifocal PVNS in children, challenging the typical understanding of the disease's localized nature.
- Recognizing diverse presentations is crucial for accurate diagnosis and management of pediatric PVNS.
- Further research into the etiology and behavior of multifocal PVNS in pediatric populations is warranted.