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Infantile myofibromatosis. A case report
1Department of Pediatric Surgery, Karadeniz Technical University Faculty of Medicine, Trabzon.
The Turkish Journal of Pediatrics
|October 1, 1995
Summary
Infantile myofibromatosis, a rare mesenchymal tumor of infancy, can cause severe complications. This case highlights intestinal perforation and obstruction, leading to fatal septicemia in a newborn.
Area of Science:
- Pediatric Pathology
- Mesenchymal Neoplasms
- Infant Health
Background:
- Infantile myofibromatosis is a rare mesenchymal tumor affecting infants.
- Tumors can develop in various tissues, including skin, muscle, bone, and viscera.
- The exact cause of infantile myofibromatosis remains unknown.
Observation:
- A newborn presented with multiple infantile myofibromatosis.
- The infant developed peritonitis and intestinal perforation.
- Surgical examination revealed intestinal tumors causing obstruction and perforation.
Findings:
- The patient underwent a jejunostomy due to intestinal perforation.
- Treatment involved total parenteral nutrition and oral feeding.
- Despite medical intervention, the infant succumbed to recurrent diarrhea and septicemia.
Implications:
- This case underscores the critical and potentially fatal complications of infantile myofibromatosis.
- Early diagnosis and management are crucial for affected infants.
- Further research into the etiology and treatment of infantile myofibromatosis is warranted.