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Thrombosed aneurysmal nonpatent ductus arteriosus: a case report
P Sattar1, J Ehrensperger, J C Ducommun
1Radiology Department, Regionalspital Biel, Vogelsang 84, CH-2502 Biel-Bienne, Switzerland.
Pediatric Radiology
|January 1, 1996
Summary
A thrombosed patent ductus arteriosus of Botallo in a newborn presented without heart murmurs but with sinus tachycardia, dyspnea, hypotonia, and hyperextension. Imaging confirmed the condition, highlighting a rare neonatal presentation.
Area of Science:
- Neonatal Medicine
- Pediatric Cardiology
- Medical Imaging
Background:
- Patent ductus arteriosus (PDA) is a common congenital heart defect.
- Aneurysmal PDA is a rare variant, and thrombosed PDA is even rarer.
- Clinical presentation can vary, especially in newborns.
Observation:
- A full-term newborn presented with generalized muscular hypotonia and hyperextension from day 1.
- Sinus tachycardia and dyspnea, particularly when in a left-sided position or drinking, emerged by day 2.
- No heart murmurs were detected initially.
Findings:
- Clinical examination and advanced imaging (radiography, ultrasound, CT, MRI) were used.
- The findings confirmed a thrombosed patent aneurysmal ductus arteriosus of Botallo.
- The absence of murmurs despite the vascular anomaly was a key observation.
Implications:
- This case highlights a rare and atypical presentation of a thrombosed PDA in a neonate.
- Early diagnosis and management are crucial for such critical congenital conditions.
- Multimodality imaging plays a vital role in characterizing complex neonatal cardiovascular anomalies.