Primary craniosynostosis: imaging features

M L Benson1, P J Oliverio, N C Yue

  • 1Department of Radiology, The Johns Hopkins Medical Institutions, Baltimore, MD 21287, USA.

Insights

Craniosynostosis, a skull growth abnormality, requires early diagnosis and imaging for optimal surgical outcomes. Computed tomography (CT) with 3D reconstruction aids in evaluating these infant skull deformities.

Area of Science:

  • Pediatric Radiology
  • Craniofacial Surgery
  • Developmental Biology

Background:

  • Craniosynostosis, defined by Virchow in 1851, involves abnormal calvarial growth, typically evident in infancy.
  • Early diagnosis and surgical intervention are crucial for improving outcomes in affected children.
  • Radiologic evaluation is essential for characterizing skull deformities and guiding surgical planning.

Purpose of the Study:

  • To illustrate the imaging findings of primary craniosynostosis.
  • To detail the nomenclature and associated abnormalities of craniosynostosis.
  • To highlight the role of CT in evaluating craniosynostosis.

Main Methods:

  • This pictorial essay reviews imaging findings from radiologic evaluations.
  • Computed tomography (CT) with three-dimensional (3D) reconstruction is emphasized.
  • The study correlates imaging findings with clinical presentation and surgical considerations.

Main Results:

  • CT with 3D reconstruction effectively visualizes the degree of sutural involvement in craniosynostosis.
  • Imaging can identify associated facial and intracranial abnormalities.
  • The essay categorizes various types of primary craniosynostosis based on imaging characteristics.

Conclusions:

  • Early and accurate diagnosis of craniosynostosis through advanced imaging is vital.
  • CT with 3D reconstruction provides comprehensive assessment for surgical planning.
  • Understanding imaging findings aids in managing diverse craniosynostosis presentations.

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