Echocardiographic diagnosis of single coronary artery in double-outlet right ventricle

S Ewing1, N H Silverman

  • 1Moffitt and Long Hospitals, University of California, San Francisco 94143, USA.

Insights

We identified a rare combination of single coronary artery and double-outlet right ventricle using echocardiography. This finding impacts surgical planning for arterial switch repairs in affected patients.

Area of Science:

  • Cardiovascular Imaging
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Double-outlet right ventricle (DORV) is a complex congenital heart defect.
  • Coronary artery anomalies can coexist with DORV, influencing surgical outcomes.
  • Accurate pre-operative diagnosis is crucial for effective management.

Purpose of the Study:

  • To report the echocardiographic diagnosis of a combined single coronary artery and DORV.
  • To highlight the initial recognition of this coronary artery variation using subcostal coronal imaging.
  • To discuss the implications for arterial switch repair in patients with this anomaly.

Main Methods:

  • Echocardiographic imaging was performed to diagnose the cardiac anomaly.
  • Subcostal coronal views were utilized for initial identification of the coronary artery variation.
  • Review of relevant literature and surgical considerations.

Main Results:

  • The echocardiographic diagnosis of single coronary artery combined with DORV was successfully made.
  • This specific coronary artery variation was initially identified in the subcostal coronal axis.
  • The combination occurs in approximately 11% of DORV patients.

Conclusions:

  • Echocardiography is effective in diagnosing combined single coronary artery and DORV.
  • Subcostal coronal imaging is valuable for identifying this coronary artery variation.
  • This anatomical combination presents significant challenges for coronary artery transfer during arterial switch repair.

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