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[Diffuse alveolar hemorrhage in Wegener's granulomatosis]
P Remiszewski1, A Broniek, K Roszkowski
1III Kliniki Gruźlicy i Chorób Płuc, Instytutu Gruźlicy i Chorób Płuc w Warszawie.
Pneumonologia I Alergologia Polska
|January 1, 1996
Summary
Two cases of Wegeners Granulomatosis presented with diffuse alveolar hemorrhage. This highlights a critical, yet uncommon, pulmonary manifestation of the disease.
Area of Science:
- Rheumatology
- Pulmonology
- Internal Medicine
Background:
- Wegeners Granulomatosis, now known as granulomatosis with polyangiitis (GPA), is a rare autoimmune vasculitis.
- Pulmonary involvement is common in GPA, but diffuse alveolar hemorrhage (DAH) is an infrequent presentation.