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Segmental multicystic kidney and ipsilateral duplication anomalies
1Department of Urology, Case Western Reserve University School of Medicine, Cleveland, Ohio 44106, USA.
The Journal of Urology
|April 1, 1996
Summary
Segmental multicystic dysplasia in newborns often presents with a duplex collecting system. Most cases can be managed nonoperatively, as the condition tends to resolve spontaneously over time.
Area of Science:
- Pediatric Urology
- Nephrology
- Medical Imaging
Background:
- Segmental multicystic dysplasia is a rare congenital anomaly.
- It involves a duplex collecting system with multicystic changes in the upper pole of the kidney.
Purpose of the Study:
- To characterize segmental multicystic dysplasia.
- To evaluate diagnostic and management strategies for this condition in neonates.
Main Methods:
- Retrospective review of three neonates diagnosed with segmental multicystic dysplasia.
- Evaluation included postnatal ultrasound, voiding cystourethrogram, and renal scan.
- Surgical and nonoperative management approaches were assessed.
Main Results:
- All patients presented with a multicystic kidney and ipsilateral orthotopic ureterocele.
- Grade V lower pole reflux was noted in all cases.
- Two patients showed reduction in segmental multicystic kidney size and reflux grade after intervention or observation.
Conclusions:
- Newborns with apparent multicystic kidney require voiding cystourethrogram and renal scan for accurate diagnosis.
- Segmental multicystic kidney often exhibits spontaneous involution and can typically be managed nonoperatively.