Intimal sarcoma of the right brachiocephalic vein presenting as the superior vena caval syndrome

A case of an 84 year old man presenting with obstruction of the superior vena cava caused by an intimal sarcoma of the right brachiocephalic vein is reported. The tumour morphology was similar to intimal sarcomas arising in major arteries, a more common primary site, and showed malignant fibrous histiocytoma-like features. Immunohistochemistry was suggestive of myofibroblastic differentiation.