Unusual appearance of intracranial fibromuscular dysplasia. A case report

D Belen1, H Bolay, M Firat

  • 1Department of Neurosurgery, Hacettepe University School of Medicine, Ankara, Turkey.

Angiology
|June 1, 1996
PubMed

Insights

This study presents a rare case of extensive intracranial fibromuscular dysplasia (FMD) causing recurrent subarachnoid hemorrhage. The findings reveal unusual angiographic features not previously reported in FMD cases.

Area of Science:

  • Neurology
  • Vascular Medicine
  • Radiology

Background:

  • Fibromuscular dysplasia (FMD) typically affects cervical arteries, with intracranial involvement being uncommon.
  • Intracranial FMD is usually confined to the internal carotid artery's intrapetrosal segment or carotid siphon.

Observation:

  • A rare case of FMD involving extensive intracranial arteries is presented.
  • The patient experienced recurrent subarachnoid hemorrhage.
  • Angiography revealed large fusiform dilatations and multiple aneurysms.

Findings:

  • The angiographic findings included widespread FMD affecting the left internal carotid artery and its major branches.
  • Involvement extended to the middle cerebral, posterior communicating, basilar, and posterior cerebral arteries.
  • This extensive and complex angiographic pattern is unprecedented for intracranial FMD.

Implications:

  • This case expands the known spectrum of intracranial fibromuscular dysplasia.
  • It highlights the importance of considering FMD in cases of unexplained subarachnoid hemorrhage with complex intracranial vascular findings.
  • Further research into the pathophysiology of extensive intracranial FMD is warranted.

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