["Malignant Kent" arrhythmia, clinical case and literature review]

The Wolff-Parkinson-White syndrome is considered as benign disorder. However, some electrophysiological properties of the accessory pathway may lead to a life-threatening affection due to rapid anterograde conduction over the accessory pathway. We report on four young patients admitted to our hospital in a haemodynamic shock. We strongly recommend to perform to all patients with preexcitation or suspected to have one, a 24 hour ambulatory ECG, an exercise stress testing and if necessary a transoesophageal electrophysiological study or an invasive electrophysiological study in order to detect patients at high risk of sudden death.