Double outlet left ventricle associated with situs inversus and atrioventricular concordance

A case is described in which the ventriculo-arterial connection of double-outlet left ventricle was associated with situs inversus and atrioventricular concordance. The case additionally exhibited l-malposition of the aorta, a subaortic ventricular septal defect, and valvar and subvalvar pulmonary stenosis. Originally diagnosed as transposition of the great arteries, a Rastelli type correction was attempted. This was not successful, owing to hypoplasia of the morphological tricuspid valve orifice.