[Renal angiomyolipomas. 9 cases (author's transl)]

Area of Science:

• Oncology
• Pathology
• Radiology

Background:

• Renal angiomyolipomas are benign mesenchymatous tumors.
• They are histologically identical whether isolated or associated with phacomatoses.
• The hypothesis that isolated angiomyolipomas represent a forme fruste of tuberous sclerosis is considered.

Observation:

• These tumors present a clinical and radiological resemblance to carcinoma, causing diagnostic confusion.
• Improved knowledge and detailed radiological analysis are crucial to avoid unexpected findings during surgery or histology.
• While inherently benign, the potential association with true malignant tumors is noted.

Findings:

• Renal angiomyolipomas can be difficult to differentiate from renal cell carcinoma pre-operatively.
• The benign nature of angiomyolipomas is established, but co-occurrence with malignancies is possible.
• Diagnostic challenges necessitate careful consideration of treatment strategies.

Implications:

• Enhanced radiological interpretation can improve diagnostic accuracy for renal angiomyolipomas.
• The potential for misdiagnosis underscores the importance of thorough pre-operative evaluation.
• Extended nephrectomy is recommended when surgical intervention is necessary due to diagnostic uncertainty.