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[Lermoyez syndrome--electrocochleographic studies]
W Maier1, N Marangos, A Aschendorff
1Hals-Nasen-Ohren-Klinik der Albert-Ludwigs-Universität Freiburg.
Laryngo- Rhino- Otologie
|June 1, 1996
Summary
Lermoyez's syndrome may not always involve endolymphatic hydrops, challenging its classification as a Meniere's disease variant. This study found normal cochlear microphonics in affected ears, suggesting different underlying pathology.
Area of Science:
- Otolaryngology
- Neurotology
- Audiology
Background:
- Lermoyez's syndrome, a rare Meniere's disease variant, is characterized by hearing improvement during vertigo.
- Existing electrocochleography data for Lermoyez's syndrome is limited to a single case.
Observation:
- Three Lermoyez's syndrome patients underwent clinical and electrocochleographic evaluation.
- Results were compared to typical Meniere's disease findings.
- Normal cochlear microphonics were observed, indicating intact hair cell function.
Findings:
- Two patients showed no elevated summating potential (SP) or SP/compound action potential (CAP) ratio.
- No hearing improvement occurred with glycerol; SP/CAP ratio remained stable during attacks.
- One patient exhibited better cochlear microphonics thresholds than pure tone thresholds.
Implications:
- Endolymphatic hydrops may not be the universal cause of Lermoyez's syndrome.
- Lermoyez's syndrome may represent a distinct condition, not merely a variant of Meniere's disease.