[Caroli's disease]

As compared with the past Caroli's disease will be more frequently diagnosed due to new examination methods. In case of clinical manifestation when the disease is confined to one lobe the possibility of lobectomy should be considered, as it is the method of choice as regards the surgical approach. It is important to emphasize the possible concurrent presence of cystic degeneration of the extrahepatic biliary pathways and renal cystosis, the possible occurrence and risk of development of cholangiocarcinoma which increases with advancing age.