Cutis marmorata telangiectatica congenita or neonatal lupus?

J M Carrascosa1, M Ribera, I Bielsa

  • 1Department of Dermatology, Hospital Universitari Germans Trias i Pujol, Universitat Autònoma de Barcelona Badalona, Spain.

Cutis marmorata telangiectatica congenita (CMTC) is a cutaneous vascular abnormality characterized by a persistent cutis marmorata pattern, spider nevuslike telangiectasia, and superficial ulceration. An infant girl was noted at birth to have characteristic features of CMTC as well as anti-Ro/SSA antibodies and a positive autonuclear antibody (ANA) test. Serologic studies carried out on her mother were positive for Ro/SSA antibodies as well as ANA (titer 1:2560). Therefore the diagnosis of neonatal lupus was made. We propose that livedo patterns mimicking CMTC might sometimes represent the residual phase of neonatal lupus active during intrauterine life.

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