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Terminal myelocystocele--a case report
1Division of Pediatric Neurosurgery, Seoul National University Children's Hospital, Korea.
Journal of Korean Medical Science
|April 1, 1996
Summary
Terminal myelocystocele, a rare spinal condition, involves herniation of the spinal cord through spina bifida. This case highlights its distinct features from myelomeningocele in infants.
Area of Science:
- Pediatric Surgery
- Neurology
- Medical Imaging
Background:
- Terminal myelocystocele is a rare congenital anomaly and a form of occult spinal dysraphism.
- It involves herniation of the hydromyelic caudal spinal cord and subarachnoid space through a posterior spina bifida.
Observation:
- A 1.5-month-old infant presented with a significant lumbosacral mass and urinary incontinence.
- Imaging and pathological findings confirmed a low-lying conus medullaris with a dilated central canal attached to subcutaneous tissue.
- Enlarged ventral subarachnoid space herniated through a sacral laminar defect.
Findings:
- The observed features were characteristic of terminal myelocystocele.
- Clinical presentation differed from myelomeningocele in several key aspects.
- The condition presented as a lumbosacral mass.
Implications:
- Terminal myelocystocele requires consideration in the differential diagnosis of congenital lumbosacral masses.
- Early recognition is crucial for appropriate management and distinguishing it from other spinal dysraphic conditions.
- Understanding its unique clinical and imaging features aids in diagnosis and patient care.