Long-term results of the Mustard procedure

Area of Science:

• Cardiology
• Pediatric Surgery
• Congenital Heart Disease

Background:

• Transposition of the great vessels (TGV) is a critical congenital heart defect.
• The Mustard procedure is a palliative surgical intervention for TGV.

Purpose of the Study:

• To evaluate the long-term outcomes of the Mustard procedure.
• To assess survival rates, functional status, and potential complications in patients undergoing this surgery.

Main Methods:

• A retrospective review of 123 patients who underwent the Mustard procedure over a 10-year period.
• Analysis of hospital mortality, late deaths, postoperative rhythm, growth, neurodevelopmental status, and catheterization findings.

Main Results:

• Hospital mortality was 10.6%, with late deaths primarily attributed to arrhythmia.
• 53% of patients maintained sinus rhythm postoperatively.
• Survivors demonstrated catch-up growth, particularly those operated on before age 2.
• Half of survivors showed comparable or improved physical and academic performance.
• Postoperative catheterization revealed residual shunts and mild obstructions in some patients.

Conclusions:

• The Mustard procedure offers survival and improved functional outcomes for TGV patients.
• Long-term monitoring is essential for managing potential complications like arrhythmias and residual obstructions.
• Early surgical intervention may enhance growth outcomes.