Long-term results of the Mustard procedure

Circulation
|September 1, 1977
PubMed

Insights

The Mustard procedure for transposition of the great vessels had a 10.6% hospital mortality. Survivors experienced significant catch-up growth and good functional outcomes, though some had residual cardiac issues.

Area of Science:

  • Cardiology
  • Pediatric Surgery
  • Congenital Heart Disease

Background:

  • Transposition of the great vessels (TGV) is a critical congenital heart defect.
  • The Mustard procedure is a palliative surgical intervention for TGV.

Purpose of the Study:

  • To evaluate the long-term outcomes of the Mustard procedure.
  • To assess survival rates, functional status, and potential complications in patients undergoing this surgery.

Main Methods:

  • A retrospective review of 123 patients who underwent the Mustard procedure over a 10-year period.
  • Analysis of hospital mortality, late deaths, postoperative rhythm, growth, neurodevelopmental status, and catheterization findings.

Main Results:

  • Hospital mortality was 10.6%, with late deaths primarily attributed to arrhythmia.
  • 53% of patients maintained sinus rhythm postoperatively.
  • Survivors demonstrated catch-up growth, particularly those operated on before age 2.
  • Half of survivors showed comparable or improved physical and academic performance.
  • Postoperative catheterization revealed residual shunts and mild obstructions in some patients.

Conclusions:

  • The Mustard procedure offers survival and improved functional outcomes for TGV patients.
  • Long-term monitoring is essential for managing potential complications like arrhythmias and residual obstructions.
  • Early surgical intervention may enhance growth outcomes.